The Prognosis for Walking in Osteogenesis Imperfecta

نویسندگان

  • KAREN DALY
  • ALISON WISBEACH
  • IGNATIUS SANPERA
  • J. A. FIXSEN
چکیده

©1996 British Editorial Society of Bone and Joint Surgery 0301-620X/96/31158 $2.00 We report a postal survey of 59 families of children with osteogenesis imperfecta. From the 51 replies we collected data on developmental milestones and walking ability and related them to the Sillence and the Shapiro classifications of osteogenesis imperfecta. Twenty-four of the patients had been treated by intramedullary rodding. Both classifications helped to predict eventual walking ability. We found that independent sitting by the age of ten months was a predictor for the use of walking as the main means of mobility with 76% attaining this. Of the patients who did not achieve sitting by ten months, walking became the main means of mobility in only 18%. The developmental pattern of mobility was similar in the rodded and non-rodded patients.

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The prognosis for walking in osteogenesis imperfecta.

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تاریخ انتشار 2004